先天性小耳畸形的研究

【作者】 庄洪兴；

【导师】 宋儒耀；

【作者基本信息】 中国协和医科大学 ， 整形外科， 1988， 博士

【摘要】 外耳、中耳和面部的多数结构由第一、第二鳃弓衍化而来，因此，由于胚胎发育上的同源性，小耳畸形常与颌面部畸形同时存在。尽管人们对这种关系的认识由来已久，但至今大多数临床学家仍把小耳畸形看作为一个单一的畸形来处理。 在我国，近年来各地相继开展了耳廓再造手术，晚近又有同期进行中耳成形术的报道，在手术设计方面进展较大，但对小耳畸形和颌面部畸形的关系至今尚未见到有关的研究报道，对第一、二鳃弓综合症缺乏足够的认识，反映在对小耳畸形的治疗上也缺乏全面考虑。 本文的研究分两部分进行：一、小耳畸形病人颅颌面部发育情况的研究；二；小耳畸形病人的治疗。更多还原

【Abstract】 In recent years, reconstruction of the auricle for the patient with microtia has been developmenting rapidly in China, but the relationship between ear and jaw defects in syndromic patterns of malformation cannot be found in Chinese literature.This study consisted of two sections, the one is about the relationshipe between ear and jaw, the other is about the comprehensive treatment for microtia.SECTION ONE The relationship between ear and jawDespite the major contributions of Grabb and Comverse et al, most clinicians and much recent writing continue to treat unilateral ear deformity as a distinct entity. The purpose of this section is to emphasize again that unilateral microtia is not a srparate syndrome but part of hemifacial microsomia. It is a research which never carried out in China befor.Materials and method.In 1986 and 1987, 138 patients with microtia who were scheduled hospital admission for ear reconstruction were studied.1, Occurrence of congenital anomalies in the family was recorded.2, The grade of microtia was graded using the system of更多还原